AVALGLUCOSIDASUM ALFA
Účinná látka · 1 přípravek na trhu
- Mezinárodní název
- AVALGLUCOSIDASUM ALFA
- Český název
- AVALGLUKOSIDASA ALFA
- Anglicky
- AVALGLUCOSIDASE ALFA
Synonyma: 1802558-87-7 · AVALGLUCOSIDASE ALFA · AVALGLUCOSIDASUM ALFA · AVALGLUKOSIDASA ALFA · MODIFIED HUMAN ACID ALFA-GLUCOSIDASE PRODUCED IN CHINESE HAMSTER OVARY (CHO) CELLS, GLYCOFORM ALFA, CONJUGATED TO A SYNTHETIC BRANCHED HEXASACCHARIDE CONTAINING TWO TERMINAL MANNOSE-6-PHOSPHATE (M6P), VIA AMINOOXY LINKERS; PREPRO-LYSOSOMAL ALFA-GLUCOSIDASE (EC=3.2.1.20) (HUMAN) (57-952)-PEPTIDE, NATURAL [ARG143,HIS167,ILE724] VARIANT, EXPRESSED IN CHO CELLS, GLYCOFORM ALFA, WITH 5~9 SIALYL END GROUPS OF GLYCAN RESIDUES BEING OXIDIZED AND CHEMICALLY MODIFIED TO 5- ACETAMIDO-3,5,7-TRIDEOXY-7-[(E)-(2-OXO-2-{2-[4-({O-(6-O-PHOSPHONO-ALFA-D-MANNOPYRANOSYL)-( 12)-O-ALFA-D-MANNOPYRANOSYL-(1->6)-O-ALFA-D-MANNOPYRANOSYL- (1->6)-O-[O-(6-O-PHOSPHONO-ALFA-D-MANNOPYRANOSYL)-(1->2)-O-ALFA-D-MANNOPYRANOSYL- (1->3)]-BETA-D-MANNOPYRANOSYL}OXY)BUTANOYL]HYDRAZINYL}ETHOXY)IMINO]-BETA-L-ARABINO-2- HEPTULO-2,6-PYRANOSYLONIC ACID GROUPS · MUTATED HUMAN ACID ALFA-GLUCOSIDASE PRODUCED IN CHINESE HAMSTER OVARY (CHO) CELLS, GLYCOFORM ALFA, CONJUGATED TO A SYNTHETIC BRANCHED HEXASACCHARIDE CONTAINING TWO TERMINAL MANNOSE-6-PHOSPHATE (M6P), VIA AMINOOXY LINKERS; [HIS^143>ARG,ARG^167>HIS,VAL^724>ILE]PREPRO-LYSOSOMAL ALFA- GLUCOSIDASE (EC=3.2.1.20) (HUMAN) (57-952)-PEPTIDE, EXPRESSED IN CHO CELLS, GLYCOFORM ALFA, WITH 5~9 SIALYL END GROUPS OF GLYCAN RESIDUES BEING OXIDIZED AND CHEMICALLY MODIFIED TO 5-ACETAMIDO-3,5,7-TRIDEOXY-7-[(E)-(2-OXO-2-{2- [4-({O-(6-O-PHOSPHONO-ALFA-D-MANNOPYRANOSYL)-(1->2)-O-ALFA- D-MANNOPYRANOSYL-(1->6)-O-ALFA-D-MANNOPYRANOSYL-(1->6)- O-[O-(6-O-PHOSPHONO-ALFA-D-MANNOPYRANOSYL)-(1->2)-O-ALFA-D-MANNOPYRANOSYL-( 1->3)]-BETA-D-MANNOPYRANOSYL} OXY)BUTANOYL]HYDRAZINYL}ETHOXY)IMINO]-BETA- L-ARABINO-2-HEPTULO-2,6-PYRANOSYLONIC ACID GROUPS. RECOMMENDED INN: LIST 79
- NEXVIADYME 100MG Prášek pro koncentrát pro infuzní roztok na předpis